Cystic adenomatoid malformation: Two clinical forms of presentation
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Keywords

Cystic adenomatoid malformation
Congenital pulmonary cystic adenomatosis
Pulmonary cystic malformation
Neonatal respiratory distress

How to Cite

1.
Gracia Remiro R, Santana Rodríguez C, Herrera Martín M, et al. Cystic adenomatoid malformation: Two clinical forms of presentation. Bol Pediatr. 2000;40(173):176-180. Accessed December 22, 2024. https://boletindepediatria.org/boletin/article/view/1245

Abstract

Cystic adenomatoid malformation (CAM) is a rare disease. It consists in an abnormal proliferation of mesenchymal lung elements secondary to maturation failure of the bronchial structures. It has a series of common pathology characteristics and others that are differentiated, and these are used to classify them. It is sometimes associated to other malformations and can be manifested clinically as: hydrops fetalis, neonatal respiratory distress, and sometimes is silent, even for long periods of time. It can be diagnosed prenatally, although the confirmation requires a pathology study of the lesion. The treatment is surgical. We present two cases of CAM with two different forms of presentation.

 

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